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Anti-neutrophil cytoplasmic antibody-associated vasculitis
ORPHA:156152
Classification level: Group of disorders- Synonym(s):
- AAV
- ANCA-associated vasculitis
- Antineutrophil cytoplasmic antibody-associated vasculitis
- Prevalence: 1-5 / 10 000
- Inheritance: -
- Age of onset: -
- ICD-10: -
- ICD-11: 4A44.A
- OMIM: -
- UMLS: C2717865
- MeSH: D056648
- GARD: -
- MedDRA: -
Summary
This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.
Detailed information
Guidelines
- Emergency guidelines
- Français (2021, pdf) - Orphanet Urgences
- Clinical practice guidelines
- Français (2019) - PNDS
- Español (2020, pdf) - Asoc Española de Pediatría
- English (2020) - Arthritis Rheumatol
- English (2020) - Orphanet J Rare Dis
- Français (2022) - PNDS


Additional information
Further information on this disease
Patient-centred resources for this disease
Research activities on this disease
Specialised Social Services
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