Orphanet: Primary cutaneous follicle center lymphoma
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Primary cutaneous follicle center lymphoma

Disease definition

A rare, indolent primary cutaneous B-cell lymphoma characterized by a solitary or grouped erythematous plaques or tumors, preferentially located on the head, neck or trunk region, and composed of centroblasts and centrocytes arranged in a follicular, diffuse, or mixed growth pattern. The lesions are smooth and typically do not ulcerate. The neoplastic cells express pan B cell markers and Bcl-6, and typically lack Bcl-2.

ORPHA:178540

Classification level: Disorder
  • Synonym(s):
    • PCFCL
  • Prevalence: -
  • Inheritance: -
  • Age of onset: -
  • ICD-10: C82.6
  • OMIM: -
  • UMLS: C1333171  C1631066
  • MeSH: -
  • GARD: -
  • MedDRA: -
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