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Paget disease of the nipple

Disease definition

Paget disease of the nipple describes a rare presentation of breast cancer, seen most frequently in women aged 50-60, manifesting with nipple drainage and itching, erythema, crusty and excoriated nipple, thickened plaques, and hyperpigmentation (less frequently). It is due to tumor cells invading the nipple-areola complex and represents 1-3% of all new breast cancer diagnoses.

ORPHA:180275

  • Synonym(s):
    • Mammary Paget disease
    • Paget disease of the breast
    • Paget's disease of the nipple
  • Prevalence: -
  • Inheritance: -
  • Age of onset: Adult
  • ICD-10: C50.0
  • OMIM: -
  • UMLS: C0030185  C1704323
  • MeSH: D010144
  • GARD: 7303
  • MedDRA: 10033367

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