Orphanet: Coats disease

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Coats disease

Disease definition

Coats disease (CD) is an idiopathic disorder characterized by retinal telangiectasia with deposition of intraretinal or subretinal exudates, potentially leading to retinal detachment and unilateral blindness. CD is classically an isolated and unilateral condition affecting otherwise healthy young children.


Classification level: Disorder
  • Synonym(s):
    • Congenital retinal telangiectasia
    • Leber miliary aneurysm
  • Prevalence: Unknown
  • Inheritance: Not applicable 
  • Age of onset: Childhood
  • ICD-10: H35.0
  • OMIM: 300216
  • UMLS: C0154832
  • MeSH: D058456
  • GARD: 6121
  • MedDRA: 10015901

Detailed information


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