Orphanet: Adenoid cystic carcinoma of the cervix uteri

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Adenoid cystic carcinoma of the cervix uteri

Disease definition

A rare, highly aggressive uterine cancer, macroscopically appearing as an irregular, slow-growing, non-friable, polypoid mass on the uterine cervix and histologically showing a pseudoglandular or cribriform growth pattern. It presents with vaginal bleeding and discharge and abdominal or pelvic pain. The tumor is highly infiltrative, often associated with vascular, lymphatic and perineural invasion, with subsequent haematogenous spread and early recurrence.


Classification level: Disorder
  • Synonym(s):
    • Cervical adenoid cystic carcinoma
  • Prevalence: -
  • Inheritance: -
  • Age of onset: -
  • ICD-10: C53.0  C53.1  C53.8
  • OMIM: -
  • UMLS: -
  • MeSH: -
  • GARD: -
  • MedDRA: -

Detailed information

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