Orphanet: Limited cutaneous systemic sclerosis

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Limited cutaneous systemic sclerosis

Disease definition

Limited cutaneous systemic sclerosis (lcSSc) is a subtype of systemic sclerosis (SSc; see this term) characterized by the association of Raynaud's phenomenon with skin fibrosis limited to the hands, face, feet and forearms.


Classification level: Subtype of disorder
  • Synonym(s):
    • Limited cutaneous systemic scleroderma
  • Prevalence: -
  • Inheritance: Multigenic/multifactorial or Not applicable 
  • Age of onset: Adult
  • ICD-10: M34.1
  • OMIM: -
  • UMLS: -
  • MeSH: -
  • GARD: 1053
  • MedDRA: -

Detailed information


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