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Neuronal intranuclear inclusion disease

Disease definition

Neuronal intranuclear inclusion disease (NIID) is a very rare multisystem neurodegenerative disorder characterized by the presence of eosinophilic intranuclear inclusions in neuronal and glial cells, and neuronal loss.


  • Synonym(s): -
  • Prevalence: Unknown
  • Inheritance: -
  • Age of onset: Childhood, Adolescent, Adult, Infancy
  • ICD-10: G31.0
  • OMIM: 603472
  • UMLS: C1863843
  • MeSH: C537395
  • GARD: 3971
  • MedDRA: -

Additional information

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