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Acute pandysautonomia

Disease definition

A rare variant of Guillain-Barré syndrome characterized by acute post-ganglionic sympathetic and parasympathetic failure presenting several weeks after acute infection with gastrointestinal symptoms (abdominal pain, vomiting, constipation, diarrhea, gastroparesis, ileus), orthostatic hypotension, erectile dysfunction, urinary frequency, urgency or retention, vasomotor instability with acrocyanosis and reduced salivation, lacrimation and sweating.

ORPHA:231457

Classification level: Disorder
  • Synonym(s):
    • Acute panautonomic GBS
    • Acute panautonomic Guillain-Barré syndrome
    • Acute panautonomic neuropathy
  • Prevalence: -
  • Inheritance: Multigenic/multifactorial or Not applicable 
  • Age of onset: All ages
  • ICD-10: G61.0
  • ICD-11: 8C01.0
  • OMIM: -
  • UMLS: C2315246
  • MeSH: -
  • GARD: -
  • MedDRA: -

  A summary on this disease is available in Español (2012) Nederlands (2012)

Additional information

Further information on this disease

Patient-centred resources for this disease

Research activities on this disease

Specialised Social Services

The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.