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Megacystis-megaureter syndrome

Disease definition

Megacystic-megaureter syndrome is an urinary tract malformation characterized by the presence of a massive primary non-obstructive vesicoureteral reflux and a large capacity, smooth, thin walled bladder due to the continual recycling of refluxed urine. Recurrent urinary infections are commonly associated with this condition.


Classification level: Disorder
  • Synonym(s):
    • Megaureter-megacystis syndrome
  • Prevalence: -
  • Inheritance: -
  • Age of onset: Infancy, Neonatal
  • ICD-10: Q62.7
  • OMIM: -
  • UMLS: C0431752
  • MeSH: -
  • GARD: -
  • MedDRA: -
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