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Disease definition

Pineoblastoma is a rare, malignant type of supratentorial primitive neuroectodermal tumor (sPNET), found mainly in children (less than 10% of cases are reported in adults), and located in the pineal region of the brain but that can metastasize along the neuroaxis. As it is the most aggressive of the pineal parenchymal tumors, it is usually associated with a poor prognosis.


Classification level: Disorder
  • Synonym(s): -
  • Prevalence: -
  • Inheritance: Not applicable 
  • Age of onset: Infancy, Childhood, Adolescent, Adult
  • ICD-10: C75.3
  • ICD-11: 2A00.20  XH1ZH1
  • OMIM: -
  • UMLS: C0205898
  • MeSH: -
  • GARD: 9369
  • MedDRA: 10050487

Detailed information


ERN produced/endorsed by ERN(s)   FSMR produced/endorsed by FSMR(s)
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