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Benign schwannoma

Disease definition

A rare benign peripheral nerve sheath tumor characterized by a usually encapsulated space-occupying lesion composed of differentiated neoplastic Schwann cells. It most commonly arises from peripheral nerves in the head and neck region and extensor aspects of the extremities, but also from spinal and cranial nerves, especially the vestibular nerve. The tumor may be asymptomatic or cause symptoms related to a mass effect. It grows slowly and only rarely undergoes malignant transformation.

ORPHA:252164

Classification level: Disorder
  • Synonym(s):
    • Neurilemmoma
    • Neurilemoma
    • Peripheral fibroblastoma
  • Prevalence: 1-9 / 100 000
  • Inheritance: Not applicable 
  • Age of onset: Adult, Elderly
  • ICD-10: D36.1
  • OMIM: -
  • UMLS: C0027809  C0854906
  • MeSH: -
  • GARD: 4767
  • MedDRA: 10029234  10029235

Detailed information

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