Orphanet: Vestibular schwannoma
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Vestibular schwannoma

Disease definition

Vestibular schwannoma is a rare tumor of the posterior fossa originating in the Schwann cells of the vestibular transitional zone of the vestibulocochlear nerve that can be benign, small, slow growing and asymptomatic or large, faster growing and aggressive and potentially fatal, presenting with symptoms of hearing and balance impairment, vertigo, ataxia, headache and fifth, sixth or seventh cranial nerve dysfunction and facial numbness.

ORPHA:252175

Classification level: Subtype of disorder
  • Synonym(s):
    • Acoustic neurilemoma
    • Acoustic neurinoma
    • Acoustic neuroma
  • Prevalence: -
  • Inheritance: -
  • Age of onset: -
  • ICD-10: D33.3
  • ICD-11: 2A02.3
  • OMIM: -
  • UMLS: C0027859
  • MeSH: -
  • GARD: 223
  • MedDRA: 10000523

Detailed information

Disease review articles

ERN : produced/endorsed by ERN(s)
FSMR : produced/endorsed by FSMR(s)
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