Orphanet: Annular atrophic lichen planus
x

Search for a rare disease

* (*) mandatory field

Other search option(s)

Suggest an update

(*) Required fields.

Attention

Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted. For all other comments, please send your remarks via contact us. Only comments written in English can be processed.

Orphanet doesn't provide personalised answers. To get in touch with the Orphanet team, please contact

Information provided in your contribution (including your email address) will be stocked in .CSV files that will be sent as an email to Orphanet's teams. These emails might be conserved in the teams' mailboxes, in our backoffice servers but will not be registered in our databases (for more information see our section General Data Protection Regulation and data privacy (GDPR) and Confidentiality).

Captcha image

Annular atrophic lichen planus

Disease definition

A rare variant of cutaneous lichen planus characterized by both annular and atrophic LP features in the same lesion.

ORPHA:254411

Classification level: Disorder
  • Synonym(s):
    • Annular atrophic LP
  • Prevalence: <1 / 1 000 000
  • Inheritance: -
  • Age of onset: Adult
  • ICD-10: L43.8
  • OMIM: -
  • UMLS: -
  • MeSH: -
  • GARD: 12676
  • MedDRA: -

Summary

Epidemiology

Fewer than ten cases have been reported in the literature.

Clinical description

Small violaceous papules develop on the trunk and extremities and are characterized by an atrophic centre and a raised hyperpigmented border. Patients are generally middle-aged and have no past history of cutaneous lesions. Histopathologically, the peripheral border has the typical features of lichen planus, while the centre of the lesion shows loss of rete ridges. There is loss of elastic fibres within the papillary dermis, both centrally and peripherally.

Etiology

Etiology is unknown.

Expert reviewer(s):  Dr Stephanie ARNOLD - Dr Susan COOPER - Last update: May 2015

  A summary on this disease is available in Deutsch (2015) Español (2015) Nederlands (2015) Português (2015) Français (2011) Italiano (2011) Greek (2011, pdf)

Additional information

Further information on this disease

Patient-centred resources for this disease

Research activities on this disease

Specialised Social Services

The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.