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Visceral calciphylaxis
Disease definition
A rare, life-threatening, non-inflammatory vasculopathy characterized by diffuse precipitation of calcium in viscera (mainly in the heart or lungs, but also in the stomach or kidneys) leading to fibrosis and thrombosis, which eventually causes tissue necrosis. Depending on the affected organ, patients may present with dyspnea, cough and respiratory failure or acute heart block and subsequent sudden cardiac death. The disease predominantly affects patients with end-stage kidney disease (ESKD) on dialysis.
ORPHA:280068
Classification level: Subtype of disorder- Synonym(s): -
- Prevalence: -
- Inheritance: -
- Age of onset: -
- ICD-10: E83.5
- ICD-11: EB90.42
- OMIM: -
- UMLS: C4749793
- MeSH: -
- GARD: -
- MedDRA: -
A summary on this disease is available in Italiano (2018) Español (2021) Français (2021) Nederlands (2021) Português (2021) Polski ()
Additional information
Further information on this disease
Patient-centred resources for this disease
Research activities on this disease
Specialised Social Services
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