Orphanet: Acute erythroid leukemia

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Acute erythroid leukemia

Disease definition

A rare unclassified acute myeloid leukemia characterized by a proliferation of immature cells exclusively of the erythroid lineage without a significant myeloblastic component. Microscopically, the cells may be undifferentiated or proerythroblastic in appearance. Patients may present with pancytopenia with fatigue, infections, and mucocutaneous bleedings, as well as weight loss, fever, and night sweats. Prognosis is poor.


Classification level: Disorder
  • Synonym(s):
    • AML M6
    • Acute myeloid leukemia M6
    • Erythroleukemia
  • Prevalence: Unknown
  • Inheritance: Not applicable 
  • Age of onset: Adult, Childhood, Adolescent, Elderly
  • ICD-10: C94.0
  • ICD-11: 2A60.35
  • OMIM: 133180
  • UMLS: C0023440
  • MeSH: -
  • GARD: 9620
  • MedDRA: -

Detailed information

General public


Disease review articles

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FSMR : produced/endorsed by FSMR(s)
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