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Classic neuroendocrine tumor of appendix

Disease definition

Classic endocrine tumor of the appendix is a type of endocrine tumor of the appendix (see this term), seen twice as frequently in females than in males, and usually presenting before the fifth decade of life. Classic endocrine tumor of the appendix is usually asymptomatic when located in the tip of the appendix (without obstruction), but acute appendicitis is often associated.


Classification level: Subtype of disorder
  • Synonym(s):
    • Classic appendiceal neuroendocrine tumor
    • Classic appendix neuroendocrine tumor
  • Prevalence: Unknown
  • Inheritance: Not applicable 
  • Age of onset: All ages
  • ICD-10: D37.3
  • OMIM: -
  • UMLS: -
  • MeSH: -
  • GARD: -
  • MedDRA: -

Detailed information


Additional information

Further information on this disease

Specialised Social Services

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