Orphanet: Double outlet right ventricle

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Double outlet right ventricle

Disease definition

A rare cono-truncal anomaly in which both the aorta and pulmonary artery originate, either entirely or predominantly, from the morphologic right ventricle.


Classification level: Disorder
  • Synonym(s):
    • DORV
  • Prevalence: 1-5 / 10 000
  • Inheritance: Multigenic/multifactorial 
  • Age of onset: Infancy, Neonatal
  • ICD-10: Q20.1
  • OMIM: 217095
  • UMLS: C0013069
  • MeSH: D004310
  • GARD: 1908
  • MedDRA: 10013611

Detailed information


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