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Vasoproliferative tumor of the retina

Disease definition

Vasoproliferative tumor of the retina is a rare, benign, retinal vascular disease characterized by solitary or multiple, unilateral or bilateral, intra-retinal tumor(s), usually located in the peripheral infero-temporal quadrant, and often associated with sub- and intraretinal exudates, epiretinal membranes, exudative retinal detachment and cystoid macular edema, as well as, occasionally, retinal and vitreous hemorrhage. Patients may present with visual loss, floaters, and/or photopsia. Association with various conditions, such as retinitis pigmentosa, congenital retinal toxoplasmosis, retinopathy of prematurity, or coloboma, has been reported.


Classification level: Disorder
  • Synonym(s):
    • Retinal vasoproliferative tumor
    • VPTR
    • Vasoproliferative tumor of the ocular fundus
  • Prevalence: -
  • Inheritance: -
  • Age of onset: -
  • ICD-10: D31.2
  • OMIM: -
  • UMLS: -
  • MeSH: -
  • GARD: -
  • MedDRA: -
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