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Stevens-Johnson syndrome

Disease definition

A limited form of Stevens-Johnson syndrome/toxic epidermal necrolysis spectrum characterized by destruction and detachment of the skin epithelium and mucous membranes involving less than 10% of the body surface area.

ORPHA:36426

Classification level: Subtype of disorder
  • Synonym(s):
    • Dermatostomatitis, Stevens Johnson type
  • Prevalence: Unknown
  • Inheritance: Not applicable 
  • Age of onset: All ages
  • ICD-10: L51.1
  • ICD-11: EB13.0
  • OMIM: 608579
  • UMLS: C0038325
  • MeSH: D013262
  • GARD: 7700
  • MedDRA: 10042033

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