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Carcinoma of esophagus, salivary gland type

Disease definition

A rare gastroesophageal tumor characterized by a typically submucosal tumor occurring usually in the middle to distal esophagus and histologically characterized as either mucoepidermoid (intimate mixture of mucus, intermediate, and epidermoid cells) or as adenoid cystic carcinoma (biphasic admixture of duct‐lining epithelial and myoepithelial cells with tubular, cribriform, solid, or basaloid growth patterns). Patients may be asymptomatic or may present with progressive dysphagia, heartburn, retrosternal pain and/or weight loss.


Classification level: Disorder
  • Synonym(s):
    • Esophageal carcinoma, salivary gland type
  • Prevalence: -
  • Inheritance: Not applicable 
  • Age of onset: Adult, Elderly
  • ICD-10: C15.0  C15.1  C15.2  C15.3  C15.4  C15.5  C15.8
  • OMIM: -
  • UMLS: C5190854
  • MeSH: -
  • GARD: -
  • MedDRA: -
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