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Carcinoma of esophagus, salivary gland type

Disease definition

A rare gastroesophageal tumor characterized by a typically submucosal tumor occurring usually in the middle to distal esophagus and histologically characterized as either mucoepidermoid (intimate mixture of mucus, intermediate, and epidermoid cells) or as adenoid cystic carcinoma (biphasic admixture of duct‐lining epithelial and myoepithelial cells with tubular, cribriform, solid, or basaloid growth patterns). Patients may be asymptomatic or may present with progressive dysphagia, heartburn, retrosternal pain and/or weight loss.

ORPHA:418945

Classification level: Disorder
  • Synonym(s):
    • Esophageal carcinoma, salivary gland type
  • Prevalence: -
  • Inheritance: Not applicable 
  • Age of onset: Adult, Elderly
  • ICD-10: C15.0  C15.1  C15.2  C15.3  C15.4  C15.5  C15.8
  • OMIM: -
  • UMLS: C5190854
  • MeSH: -
  • GARD: -
  • MedDRA: -

  A summary on this disease is available in Español (2018) Français (2018) Italiano (2018) Nederlands (2018)

Additional information

Further information on this disease

Patient-centred resources for this disease

Research activities on this disease

Specialised Social Services

The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.