Orphanet: Mucous membrane pemphigoid

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Mucous membrane pemphigoid

Disease definition

A rare autoimmune bullous skin disease characterized clinically by blistering of the mucous membranes followed by scarring, and immunologically characterized by IgG, IgA and/or C3 deposits on the epidermal basement membrane. The disease principally involves the oral mucosa, but may also affect ocular, pharyngolaryngeal, genital, and esophageal mucous membranes.


Classification level: Disorder
  • Synonym(s):
    • Cicatricial pemphigoid
    • Mucosal pemphigoid
    • Mucosynechial pemphigoid
  • Prevalence: Unknown
  • Inheritance: Not applicable 
  • Age of onset: Adult, Elderly, Infancy, Childhood, Adolescent
  • ICD-10: L12.1
  • OMIM: 164185
  • UMLS: C0030804
  • MeSH: -
  • GARD: 5913
  • MedDRA: 10057052

Detailed information


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