Orphanet: Fatal familial insomnia

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Fatal familial insomnia

Disease definition

Fatal familial insomnia (FFI) is a very rare form of prion disease (see this term) characterized by subacute onset of insomnia showing as a reduced overall sleep time, autonomic dysfunction, and motor disturbances.

ORPHA:466

Classification level: Disorder

Synonym(s): -
Prevalence: <1 / 1 000 000
Inheritance: Autosomal dominant
Age of onset: Adult
ICD-10: A81.8
OMIM: 600072
UMLS: C0206042
MeSH: D034062
GARD: 6429
MedDRA: 10072077

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Fatal familial insomnia

ORPHA:466

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