Orphanet: Posterior cortical atrophy

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Posterior cortical atrophy

Disease definition

Posterior Cortical Atrophy (PCA) is a rare progressive neurodegenerative disorder with a typical onset between 50-65 years of age characterized by progressive impairment of higher visual processing skills and other posterior cortical functions without any evidence of ocular abnormalities.


Classification level: Disorder
  • Synonym(s):
    • Benson syndrome
    • Biparietal Alzheimer disease
    • PCA
  • Prevalence: Unknown
  • Inheritance: Unknown 
  • Age of onset: Adult
  • ICD-10: G31.1
  • OMIM: -
  • UMLS: -
  • MeSH: -
  • GARD: -
  • MedDRA: -

Detailed information


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