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Pulmonary blastoma

Disease definition

A biphasic primary lung neoplasm, belonging to the group of sarcomatoid lung carcinomas (SLCs). The tumor contains both an epithelial well-differentiated component, showing tubular architecture resembling the normal fetal lung, and a mesenchymal undifferentiated stroma with a so-called ''blastema-like'' configuration that resembles an embryonic lung.

ORPHA:64741

Classification level: Disorder
  • Synonym(s):
    • Pneumoblastoma
  • Prevalence: Unknown
  • Inheritance: Multigenic/multifactorial 
  • Age of onset: Adult
  • ICD-10: C34.1  C34.2  C34.3  C34.8  C34.9
  • OMIM: -
  • UMLS: C0206629
  • MeSH: D018202
  • GARD: -
  • MedDRA: -

Detailed information

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