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Multiple endocrine neoplasia type 1

Disease definition

A rare inherited cancer syndrome, characterized by the development of multiple neuroendocrine tumors of the parathyroids, gastro-entero-pancreatic tract, and anterior pituitary gland, and less commonly the adrenal cortical gland, thymus and bronchi, with other non-endocrine tumors in some patients.

ORPHA:652

Classification level: Disorder
  • Synonym(s):
    • MEN1
    • Wermer syndrome
  • Prevalence: 1-9 / 100 000
  • Inheritance: Autosomal dominant or Not applicable 
  • Age of onset: All ages
  • ICD-10: D44.8
  • OMIM: 131100
  • UMLS: C0025267
  • MeSH: D018761
  • GARD: 3829
  • MedDRA: 10028190

Detailed information

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