Orphanet: Nephroblastoma

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Disease definition

A rare malignant renal tumor, typically affecting the pediatric population, characterized by an abnormal proliferation of cells that resemble the kidney cells of an embryo (metanephroma), leading to the term embryonal tumor.


Classification level: Disorder
  • Synonym(s):
    • Renal embryonic tumor
    • Wilms tumor
  • Prevalence: 1-9 / 100 000
  • Inheritance: Autosomal dominant or Not applicable 
  • Age of onset: Childhood
  • ICD-10: C64
  • OMIM: 194070  194071  194090  601363  601583  616806
  • UMLS: C0027708
  • MeSH: D009396
  • GARD: 7892
  • MedDRA: 10029145

Detailed information

Article for general public


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