Orphanet: Polycythemia vera

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Polycythemia vera

Disease definition

Polycythemia vera (PV) is an acquired myeloproliferative disorder characterized by an elevated absolute red blood cell mass caused by uncontrolled red blood cell production, frequently associated with uncontrolled white blood cell and platelet production.


Classification level: Disorder
  • Synonym(s):
    • Acquired primary erythrocytosis
    • Osler-Vaquez disease
    • PV
    • Polycythemia rubra vera
    • Vaquez disease
  • Prevalence: 1-5 / 10 000
  • Inheritance: Not applicable 
  • Age of onset: All ages
  • ICD-10: D45
  • OMIM: 263300
  • UMLS: C0032463
  • MeSH: D011087
  • GARD: 7422
  • MedDRA: 10036057

Detailed information

Article for general public


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