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Sporadic idiopathic steroid-resistant nephrotic syndrome

Disease definition

Steroid-resistant, sporadic idiopathic nephrotic syndrome, is a heterogeneous entity. Nephrotic syndrome is characterised by marked proteinuria, with reduced plasmatic levels of albumin, and potentially with oedema.


  • Synonym(s):
    • Sporadic idiopathic nephrosis
  • Prevalence: Unknown
  • Inheritance: Not applicable 
  • Age of onset: Childhood
  • ICD-10: N04.1  N04.3  N04.8
  • OMIM: 612551
  • UMLS: -
  • MeSH: -
  • GARD: -
  • MedDRA: -

Detailed information

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Additional information

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