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Enthesitis-related juvenile idiopathic arthritis

Disease definition

A rare inflammatory rheumatic disease in a child younger than 16 years characterized by arthritis and/or enthesitis and/or acute anterior uveitis. The most commonly affected joints at diagnosis are the knees, ankles, and hips. The small joints of the feet and toes are also often involved.

ORPHA:85438

Classification level: Disorder
  • Synonym(s):
    • Enthesitis-related JIA
    • Juvenile ERA
  • Prevalence: 1-9 / 100 000
  • Inheritance: Unknown 
  • Age of onset: Childhood, Adolescent
  • ICD-10: M08.8
  • OMIM: -
  • UMLS: C3495919
  • MeSH: -
  • GARD: 10969
  • MedDRA: -
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