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Myoclonic epilepsy in non-progressive encephalopathies

Disease definition

Myoclonic epilepsy in non-progressive encephalopathies is a rare epilepsy syndrome characterized by recurrent, long-lasting myoclonic status in infants and young children with a non-progressive encephalopathy, associated with transient and recurring motor, cognitive and/or behavioral disturbances.


Classification level: Disorder
  • Synonym(s):
    • Myoclonic status in non-progressive encephalopathies
    • Myoclonus epilepsy in non-progressive encephalopathies
  • Prevalence: Unknown
  • Inheritance: -
  • Age of onset: Infancy, Childhood
  • ICD-10: G40.4
  • OMIM: -
  • UMLS: -
  • MeSH: -
  • GARD: -
  • MedDRA: -
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