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Desmoid tumor

Disease definition

A desmoid tumor (DT) is a benign, locally invasive soft tissue tumor associated with a high recurrence rate but with no metastatic potential.


Classification level: Disorder
  • Synonym(s):
    • Aggressive fibromatosis
    • Desmoid type fibromatosis
  • Prevalence: Unknown
  • Inheritance: Not applicable or Unknown 
  • Age of onset: Adolescent, Adult
  • ICD-10: D48.1
  • OMIM: 135290
  • UMLS: C0079218
  • MeSH: -
  • GARD: 1820
  • MedDRA: -

Detailed information


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