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Posterior urethral valve

Disease definition

Posterior urethral valve (PUV) is the most common anomaly of fetal lower urinary tract obstruction (LUTO)and is characterized by an abnormal congenital obstructing membrane that is located within the posterior urethra associated with significant obstruction of the male bladder restricting normal bladder emptying.


  • Synonym(s):
    • PUV
  • Prevalence: 1-9 / 100 000
  • Inheritance: Not applicable 
  • Age of onset: Antenatal, Neonatal
  • ICD-10: Q64.2
  • OMIM: -
  • UMLS: C0238506  C0542520
  • MeSH: -
  • GARD: 7439
  • MedDRA: 10036369

Additional information

Specialised Social Services

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