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Disease definition

A rare, congenital non-syndromic heart malformation characterized by an atypical location of the heart in a central position in the thorax, with the apex in the midline of the thorax. Atria are usually situs solitus, whereas ventricles may be situs inversus. Various congenital heart anomalies and visceral situs inversus have also been associated.


Classification level: Disorder
  • Synonym(s):
    • Midline heart
  • Prevalence: -
  • Inheritance: -
  • Age of onset: -
  • ICD-10: Q24.8
  • OMIM: -
  • UMLS: C0265865
  • MeSH: -
  • GARD: -
  • MedDRA: -
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