Orphanet: Stevens Johnson syndrome/toxic epidermal necrolysis spectrum

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Stevens-Johnson syndrome/toxic epidermal necrolysis spectrum

Disease definition

Toxic epidermal necrolysis (TEN) is an acute and severe skin disease with clinical and histological features characterized by the destruction and detachment of the skin epithelium and mucous membranes.


Classification level: Disorder
  • Synonym(s):
    • SJS-TEN
    • Toxic epidermolysis
  • Prevalence: Unknown
  • Inheritance: Not applicable 
  • Age of onset: All ages
  • ICD-10: L51.2
  • OMIM: 608579
  • UMLS: C0014518
  • MeSH: D004816
  • GARD: 7743
  • MedDRA: 10044223

Detailed information


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