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Disease definition

A rare, congenital, non-syndromic, developmental defect during embryogenesis characterized by the heart located in the normal (levo) position associated with abdominal viscera located in the dextro position. Cardiac (e.g. interrupted inferior vena cava with azygous continuation) and/or splenic (asplenia, polysplenia) anomalies, as well as intestinal malrotation, are frequently associated.


Classification level: Disorder
  • Synonym(s):
    • Isolated levocardia
    • Levocardia with situs inversus
  • Prevalence: -
  • Inheritance: -
  • Age of onset: -
  • ICD-10: Q24.1
  • OMIM: -
  • UMLS: C0023569
  • MeSH: D007979
  • GARD: -
  • MedDRA: 10071015

Additional information

Further information on this disease

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