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Acute myeloblastic leukemia without maturation
Disease definition
A rare, acute myeloid leukemia characterized by no significant myeloid maturation and more than 90% blast cells in the non-erythroid population. Various degrees of anemia, thrombocytopenia, or pancytopenia are present. Frequent clinical manifestations include fatigue, fever, bleeding disorders, and organomegaly, especially hepatosplenomegaly.
ORPHA:98833
Classification level: Disorder- Synonym(s):
- AML M1
- Acute myeloblastic leukemia M1
- Prevalence: -
- Inheritance: -
- Age of onset: Adult
- ICD-10: C92.0
- OMIM: -
- UMLS: C0026998
- MeSH: -
- GARD: 526
- MedDRA: -
Detailed information
Article for general public
Professionals
- Review article
- English (2008)
- Deutsch (2017)
- Clinical practice guidelines
- English (2012)
Additional information
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