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Thiel-Behnke corneal dystrophy

Disease definition

Thiel-Behnke corneal dystrophy (TBCD) is a rare form of superficial corneal dystrophy characterized by sub-epithelial honeycomb-shaped corneal opacities in the superficial cornea, and progressive visual impairment.


Classification level: Disorder
  • Synonym(s):
    • Anterior limiting membrane dystrophy type 2
    • Anterior limiting membrane dystrophy type II
    • Corneal dystrophy of Bowman layer type 2
    • Corneal dystrophy of Bowman layer type II
    • Curly fiber corneal dystrophy
    • Honeycomb corneal dystrophy
    • TBCD
    • Waardenburg-Jonker corneal dystrophy
  • Prevalence: Unknown
  • Inheritance: Autosomal dominant 
  • Age of onset: Adolescent, Childhood, Adult
  • ICD-10: H18.5
  • ICD-11: 9A70.Y
  • OMIM: 602082
  • UMLS: C1562894
  • MeSH: C535942
  • GARD: 9275
  • MedDRA: -

Detailed information

Disease review articles

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The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.