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Granular corneal dystrophy type I

Disease definition

Type I granular corneal dystrophy (GCDI) is a rare form of stromal corneal dystrophy (see this term) characterized by multiple small deposits in the superficial central corneal stroma, and progressive visual impairment, which may sometimes be severe.


Classification level: Disorder
  • Synonym(s):
    • Classic GCD
    • Classic granular corneal dystrophy
    • Corneal dystrophy Groenouw type I
    • GCD1
    • GCDI
    • Granular corneal dystrophy type 1
  • Prevalence: Unknown
  • Inheritance: Autosomal dominant 
  • Age of onset: Childhood
  • ICD-10: H18.5
  • OMIM: 121900
  • UMLS: C1641846
  • MeSH: -
  • GARD: 9677
  • MedDRA: -

Detailed information


Additional information

Further information on this disease

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