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Reticular dystrophy of the retinal pigment epithelium

Disease definition

Reticular dystrophy of the retinal pigment epithelium is a patterned dystrophy of the retinal pigment epithelium (see this term), of progressive course, characterized by the presence of a bilateral hyperpigmented reticular pattern resembling a fishnet with knots, resulting in a slowly progressive loss of vision that often only becomes apparent in old age. Reticular dystrophy of the retinal pigment epithelium is sometimes associated with scleral staphyloma, choroidal neovascularization, convergent strabismus, spherophakia with myopia and luxated lenses, and partial atrophy of the iris.


  • Synonym(s): -
  • Prevalence: -
  • Inheritance: Unknown or Autosomal recessive 
  • Age of onset: Adult
  • ICD-10: H35.5
  • OMIM: 179840  267800  617175
  • UMLS: C1867332
  • MeSH: -
  • GARD: -
  • MedDRA: -

Additional information

Further information on this disease

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