Orphanet: Maligant granulosa cell tumor of the ovary

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Maligant granulosa cell tumor of the ovary

Disease definition

Malignant granulosa cell tumor of ovary is a rare malignant sex cord stromal tumor of ovary (see this term) arising from the granulosa cells of the ovary, which occurs in peri and post menopausal women, and that presents with abnormal vaginal bleeding, abdominal pain and distension. The tumor is frequently unilateral, estrogen secreting, and has a slow natural history and a tendency to relapse long after the initial diagnosis, necessitating prolonged follow-up.


Classification level: Disorder
  • Synonym(s):
    • Granulosa cell cancer
    • Granulosa cell malignant tumor
  • Prevalence: -
  • Inheritance: -
  • Age of onset: Adult, Elderly, Adolescent
  • ICD-10: C56
  • OMIM: -
  • UMLS: C0334401  C1567257
  • MeSH: D006106
  • GARD: -
  • MedDRA: -

Detailed information

Article for general public


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