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Malignant Sertoli-Leydig cell tumor of the ovary

Disease definition

A rare malignant sex cord stromal tumor of ovary occuring typically in young women and characterized by manifestations of androgen excess (hirsutism, hair loss, amenorrhea, or oligomenorrhea), when functional.


Classification level: Disorder
  • Synonym(s):
    • Androblastoma
    • Arrhenoblastoma
    • Ovarian Sertoli-Leydig cell cancer
    • Ovarian malignant Sertoli-Leydig cell tumor
    • Virilizing ovarian tumor
  • Prevalence: -
  • Inheritance: -
  • Age of onset: Adult, Elderly, Childhood, Adolescent
  • ICD-10: C56
  • ICD-11: 2C73.Y
  • OMIM: -
  • UMLS: -
  • MeSH: -
  • GARD: 5495
  • MedDRA: -

Detailed information

General public


  • Clinical practice guidelines
  • English (2012) - J Pediatr Hematol Oncol
ERN : produced/endorsed by ERN(s)
FSMR : produced/endorsed by FSMR(s)
The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.