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Malignant Sertoli-Leydig cell tumor of the ovary

Disease definition

A rare malignant sex cord stromal tumor of ovary occuring typically in young women and characterized by manifestations of androgen excess (hirsutism, hair loss, amenorrhea, or oligomenorrhea), when functional.

ORPHA:99916

Classification level: Disorder
  • Synonym(s):
    • Androblastoma
    • Arrhenoblastoma
    • Ovarian Sertoli-Leydig cell cancer
    • Ovarian malignant Sertoli-Leydig cell tumor
    • Virilizing ovarian tumor
  • Prevalence: -
  • Inheritance: -
  • Age of onset: Adult, Elderly, Childhood, Adolescent
  • ICD-10: C56
  • ICD-11: 2C73.Y
  • OMIM: -
  • UMLS: -
  • MeSH: -
  • GARD: 5495
  • MedDRA: -

  A summary on this disease is available in Español (2014) Italiano (2014) Nederlands (2014)

Detailed information

General public

Guidelines

  • Clinical practice guidelines
  • English (2012) - J Pediatr Hematol Oncol
ERN : produced/endorsed by ERN(s)
FSMR : produced/endorsed by FSMR(s)

Additional information

Further information on this disease

Patient-centred resources for this disease

Research activities on this disease

Specialised Social Services

The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.