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Semantic dementia

Disease definition

Semantic dementia (SD) is a form of frontotemporal dementia (FTD; see this term), characterized by the progressive, amodal and profound loss of semantic knowledge (combination of visual associative agnosia, anomia, surface dyslexia or dysgraphia and disrupted comprehension of word meaning) and behavioral abnormalities, attributable to the degeneration of the anterior temporal lobes.

ORPHA:100069

Classification level: Disorder
  • Synonym(s):
    • Semantic primary progressive aphasia
    • Semantic variant PPA
  • Prevalence: -
  • Inheritance: Multigenic/multifactorial or Not applicable 
  • Age of onset: Adult
  • ICD-10: G31.0
  • ICD-11: 6D83
  • OMIM: 172700  600274
  • UMLS: C0338462
  • MeSH: -
  • GARD: 10792
  • MedDRA: -

  A summary on this disease is available in Español (2014) Français (2014) Nederlands (2014)

Detailed information

General public

Guidelines

ERN produced/endorsed by ERN(s)   FSMR produced/endorsed by FSMR(s)

Additional information

Further information on this disease

Patient-centred resources for this disease

Research activities on this disease

Specialised Social Services

The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.