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Neuroendocrine neoplasm of appendix

Disease definition

A rare sporadic neoplasm of the appendix and the second most common type of digestive endocrine tumor, often with no specific clinical presentation. They are divided into either classic endocrine tumor of the appendix or the more aggressive goblet cell carcinoma (GCC).


Classification level: Disorder
  • Synonym(s):
    • Appendiceal NEN
    • Appendiceal neuroendocrine neoplasm
    • NEN of appendix
  • Prevalence: -
  • Inheritance: -
  • Age of onset: Adult
  • ICD-10: C18.1  D37.3
  • ICD-11: 2B81.2
  • OMIM: -
  • UMLS: C1879718
  • MeSH: -
  • GARD: -
  • MedDRA: -

Detailed information


ERN produced/endorsed by ERN(s)   FSMR produced/endorsed by FSMR(s)
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