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Neuroendocrine neoplasm of appendix

Disease definition

Endocrine tumor of the appendix is the most common sporadic neoplasm of the appendix and the second most common type of digestive endocrine tumor, often with no specific clinical presentation. They are divided into either classic endocrine tumor of the appendix or the more aggressive goblet cell carcinoma (GCC; see these terms).

ORPHA:100079

Classification level: Disorder
  • Synonym(s):
    • Appendiceal NEN
    • Appendiceal neuroendocrine neoplasm
    • NEN of appendix
  • Prevalence: -
  • Inheritance: -
  • Age of onset: -
  • ICD-10: C18.1  D37.3
  • OMIM: -
  • UMLS: -
  • MeSH: -
  • GARD: -
  • MedDRA: -

Detailed information

Professionals

The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.