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Autoimmune pancreatitis

Disease definition

A rare pancreatic disease characterized by chronic non-alcoholic pancreatitis that presents with abdominal pain, steatorrhea, obstructive jaundice and responds well to steroid therapy and is seen in two subforms: type which affects elderly males, involves other organs and has increased immunoglobin G4 (IgG4) levels and type 2 which affects both sexes equally but presents at a younger age and has no other organ involvement or increased IgG4 levels.


Classification level: Group of disorders
  • Synonym(s):
    • AIP
  • Prevalence: -
  • Inheritance: Not applicable 
  • Age of onset: -
  • ICD-10: K86.1
  • ICD-11: DC33
  • OMIM: -
  • UMLS: C2609129
  • MeSH: -
  • GARD: 10911
  • MedDRA: 10069002

Detailed information

Article for general public


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