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Primary cutaneous amyloidosis
Disease definition
A rare group of skin diseases characterized histologically by the extracellular accumulation of amyloid deposits in the dermis. Rare forms include lichen amyloidosus, X-linked reticulate pigmentary disorder, primary localized cutaneous nodular amyloidosis, and macular amyloidosis.
ORPHA:137807
Classification level: Group of disordersAdditional information
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