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Primary cutaneous amyloidosis

Disease definition

A rare group of skin diseases characterized histologically by the extracellular accumulation of amyloid deposits in the dermis. Rare forms include lichen amyloidosus, X-linked reticulate pigmentary disorder, primary localized cutaneous nodular amyloidosis, and macular amyloidosis.


Classification level: Group of disorders
  • Synonym(s):
    • PLCA
    • Primary localized cutaneous amyloidosis
  • Prevalence: Unknown
  • Inheritance: Autosomal dominant or Not applicable 
  • Age of onset: All ages
  • ICD-10: -
  • ICD-11: 5D00.0
  • OMIM: -
  • UMLS: C0268397
  • MeSH: -
  • GARD: 132
  • MedDRA: 10011659
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