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Carney triad

Disease definition

A rare non-hereditary condition characterized by gastrointestinal stromal tumors (GIST, intramural mesenchymal tumors of the gastrointestinal tract with neuronal or neural crest cell origin), pulmonary chondromas and extraadrenal paragangliomas.


  • Synonym(s): -
  • Prevalence: <1 / 1 000 000
  • Inheritance: -
  • Age of onset: Adolescent, Adult
  • ICD-10: D44.8
  • OMIM: 604287
  • UMLS: C1858592
  • MeSH: -
  • GARD: 10924
  • MedDRA: -
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