Search for a rare disease
Other search option(s)
Acquired hemophagocytic lymphohistiocytosis associated with malignant disease
Disease definition
A rare, secondary hemophagocytic lymphohistiocytosis characterized by occurring as either initial presentation of a malignant disease or at any stage during chemotherapy. The common associated malignancies are lukemias, B-cell, T-cell or NK-cell lymphomas, and Hodgkin lymphoma. Typical clinical manifestation includes fever, hepatosplenomegaly and cytopenias, combined with specific laboratory findings.
ORPHA:158057
Classification level: Disorder- Synonym(s): -
- Prevalence: Unknown
- Inheritance: -
- Age of onset: All ages
- ICD-10: D76.1
- ICD-11: 3B62.Y
- OMIM: -
- UMLS: -
- MeSH: -
- GARD: -
- MedDRA: -
A summary on this disease is available in Español (2018) Français (2018) Italiano (2018) Nederlands (2018) Polski ()
Detailed information
Disease review articles
- Review article
- Deutsch (2020) - Onkopedia


Additional information
Further information on this disease
Patient-centred resources for this disease
Research activities on this disease
Specialised Social Services
The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.