Orphanet: Aortic arch interruption

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Aortic arch interruption

Disease definition

A rare heart defect characterized by complete lack of anatomical continuity between the transverse aortic arch and the descending thoracic aorta. AAI should be distinguished anatomically from atresia of the aortic arch where continuity between these segments is achieved by an imperforate fibrous strand of various lengths.

ORPHA:2299

Classification level: Disorder

Synonym(s): -
Prevalence: Unknown
Inheritance: Not applicable
Age of onset: Infancy, Neonatal
ICD-10: Q25.4
ICD-11: LA8B.22
OMIM: -
UMLS: C0152419
MeSH: -
GARD: 740
MedDRA: 10022599

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Aortic arch interruption

ORPHA:2299

A summary on this disease is available in Español (2015) Français (2015) Italiano (2015) Nederlands (2015) Deutsch (2004) Português (2004)

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