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Ectopic aldosterone-producing tumor

Disease definition

Ectopic aldosterone-producing tumor is an extremely rare aldosterone-producing neoplasm composed of aberrant adrenocortical tissue located outside the adrenal glands (e.g. in retroperitoneum, perirenal or periaortic fatty tissue, thorax, spinal canal, testes, ovaries) typically characterized by symptoms related to increased aldosterone levels (such as sustained, treatment-resistant hypertension and hypokalemia) or symptoms caused by local tumor enlargement.


Classification level: Disorder
  • Synonym(s):
    • Extra-adrenal aldosterone-producing tumor
  • Prevalence: -
  • Inheritance: Not applicable 
  • Age of onset: All ages
  • ICD-10: E26.8
  • OMIM: -
  • UMLS: C4755311
  • MeSH: -
  • GARD: -
  • MedDRA: -

Detailed information


  • Clinical practice guidelines
  • English (2016) - J Clin Endocrinol Metab
ERN produced/endorsed by ERN(s)   FSMR produced/endorsed by FSMR(s)
The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.