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Idiopathic intracranial hypertension

Disease definition

Idiopathic intracranial hypertension is a neurological disorder characterized by isolated increased intracranial pressure manifesting with recurrent and persistent headaches, nausea, vomiting, progressive and transient obstruction of the visual field, papilledema. Visual loss can be irreversible.


  • Synonym(s):
    • Benign intracranial hypertension
    • IIH
    • Pseudotumor cerebri
  • Prevalence: 1-5 / 10 000
  • Inheritance: -
  • Age of onset: Adult, Elderly
  • ICD-10: G93.2
  • OMIM: 243200
  • UMLS: C0033845
  • MeSH: -
  • GARD: 4561
  • MedDRA: -

Detailed information


Additional information

Further information on this disease

Specialised Social Services

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